Author:
Kaur Balwinder,Kaur Parneet,Kaur Khushpreet,Mittal Princy
Abstract
ABSTRACT
Pentalogy of Cantrell is a rare multiple congenital malformation syndrome characterized by combination of five features: abdominal wall defect, defect of lower sternum, defect of diaphragmatic pericardium, defect of anterior diaphragm and congenital cardiac anomalies. These defects can be diagnosed as early as 1st trimester of pregnancy. The complexity of these anomalies, in particular the presence of cardiac defects, determines the management as well as prognosis.
How to cite this article
Kaur P, Kaur K, Kaur B, Mittal P. Pentalogy of Cantrell: A Rare Multiple Congenital Malformation Syndrome. J South Asian Feder Obst Gynae 2015;7(3):210-212.
Publisher
Jaypee Brothers Medical Publishing
Subject
Obstetrics and Gynecology
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