Serial Audiometry and Speech Recognition Findings in Finnish Usher Syndrome Type III Patients

Author:

Plantinga R.F.,Kleemola L.,Huygen P.L.M.,Joensuu T.,Sankila E.-M.,Pennings R.J.E.,Cremers C.W.R.J.

Publisher

S. Karger AG

Subject

Speech and Hearing,Sensory Systems,Otorhinolaryngology,Physiology

Reference20 articles.

1. Stable and Progressive Hearing Loss in Type 2A Usher's Syndrome

2. USH3A transcripts encode clarin-1, a four-transmembrane-domain protein with a possible role in sensory synapses

3. Progressive hearing loss, hypoplasia of the cochlea and widened vestibular aqueducts are very common features in Pendred’s syndrome

4. Davenport SLH, Omenn GS: The heterogeneity of Usher syndrome; in Littlefield JW, Ebbing FJG, Henderson JW (eds): Fifth International Conference on Birth Defects. Amsterdam, Excerpta Medica, 1977, pp 87-88.

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