Affiliation:
1. Regional Clinical Hospital No. 2
2. Pacific State Medical University
Abstract
The anterior segment mesenchymal dysgenesis is a failure of the normal development of the anterior structures of the eye caused by mutations in the PAX6 gene REIG1, PITX2 and B3GLCT, BMP4, CYP1B1, FOXC1, FOXE3, GJA1, PXDN TP63, and PAX6. Disorders in the structure of these genes or their interactions lead to gross developmental disorders. In this article, we describe a clinical case of an early stepped surgical treatment of Peters anomaly in a child from 1 to 17 years old. According to the presented clinical case and those reported in scientific literature, conservative treatment of this pathology is yet to be developed. At the same time, surgical intervention in the form of penetrating keratoplasty is often fraught with unpredictability and unacceptable postoperative results.
Publisher
Pacific State Medical University
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