Microangiopathy of Brain, Retina, and Inner Ear (Susac’s Syndrome) in an Adolescent Female Presenting as Acute Disseminated Encephalomyelitis-Reference-Cited by-同舟云学术

Microangiopathy of Brain, Retina, and Inner Ear (Susac’s Syndrome) in an Adolescent Female Presenting as Acute Disseminated Encephalomyelitis

Published:2004-07-01 Issue:1 Volume:114 Page:276-281
ISSN:0031-4005
Container-title:Pediatrics
language:en
Short-container-title:

Author:

Hahn Jin S.¹²³,Lannin W. Craig⁴,Sarwal Minnie M.²³

Affiliation:

1. Departments of Neurology

2. Pediatrics, Stanford University School of Medicine, Stanford, California

3. Lucile Packard Children’s Hospital, Palo Alto, California

4. Lucile Packard Children’s Hospital, Redding, California

Abstract

Susac’s syndrome is a rare disorder that consists of microangiopathy of the brain, retina, and inner ear and usually affects young women in young adulthood. The triad of clinical manifestations consists of acute encephalopathy with neurologic signs, branch retinal artery occlusion (BRAO), and sensorineural hearing loss. We present a case of an adolescent female who presented at age 16 years with clinical and neuroimaging features of acute disseminated encephalomyelitis (ADEM). The full triad did not develop until 2.5 years after the initial neurologic presentation.

Publisher

American Academy of Pediatrics (AAP)

Subject

Pediatrics, Perinatology and Child Health

Link

https://publications.aap.org/pediatrics/article-pdf/114/1/276/1005810/zpe00704000276.pdf

Reference13 articles.

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