Anesthetic management of a parturient with spondylocostal dysostosis (Jarcho-Levin syndrome) for cesarean delivery

Abstract

Jarcho Levin syndrome was first described by Saul Jarcho and Paul Levin in 1938. The syndrome is characterized by multiple skeletal deformities due to axial skeletal developmental defects during the embryologic stage. Generalized vertebral defects include fused, missing, or deformed vertebrae, and these are seen throughout the cervical, thoracic, and lumbar spine. The patients have short stature and kyphoscoliosis. In pregnancy, these skeletal defects may have pronounced effects on the parturient and the baby, so special considerations are needed by the obstetricians as well as the obstetric anesthesiologists. This case report highlights the challenges our anesthesiology team faces while providing patient care and points out the different anesthetic management approaches that can be used in cesarean delivery for parturients with spondylocostal dysostosis. Key words: Jarcho-Levin Syndrome; Anesthesia; Congenital; Hereditary; Abnormalities; Growth Disorders; Physical Appearance Citation: Ibrahim MA, Almetwalli RR. Anesthetic management of a parturient with spondylocostal dysostosis (Jarcho-Levin syndrome) for cesarean delivery. Anaesth. pain intensive care 2023;27(6):780−782; DOI: 10.35975/apic.v27i6.2353 Received: September 02, 2023; Reviewed: October 25, 2023; Accepted: November 01, 2023