Experience of using specialized mixture of enteral nutrition in children with nutritive deficiency in cystic fibrosis

Abstract

Сystic fibrosis is an autosomal recessive hereditary multisystem disease which is characterized by severe exocrine pancreatic insufficiency, chronic lung disease, and protein-energy malnutrition. Some studies have indicated that the body mass index is an independent factor which adversely affected survival of patients with cystic fibrosis. There is a direct correlation between body mass index, lung function and life expectancy. Objective. To determine the effectiveness and tolerability of the product for children’s dietary nutrition ‘NUTRINIdrink with dietary fibre (neutral taste)’ for children over one year of age for enteral nutrition in cystic fibrosis complicated by protein-energy deficiency.