Impact of Pathogenic FBN1 Variant Types on the Progression of Aortic Disease in Patients With Marfan Syndrome

Author:

Takeda Norifumi1,Inuzuka Ryo2,Maemura Sonoko1,Morita Hiroyuki1,Nawata Kan3,Fujita Daishi1,Taniguchi Yuki4,Yamauchi Haruo3,Yagi Hiroki1,Kato Masayoshi1,Nishimura Hiroshi1,Hirata Yoichiro2,Ikeda Yuichi1,Kumagai Hidetoshi15,Amiya Eisuke1,Hara Hironori1,Fujiwara Takayuki1,Akazawa Hiroshi1,Suzuki Jun-ichi15,Imai Yasushi67,Nagai Ryozo8,Takamoto Shinichi9,Hirata Yasunobu10,Ono Minoru3,Komuro Issei1

Affiliation:

1. Department of Cardiovascular Medicine (N.T., S.M., H.M., D.F., H. Yagi, M.K., H.N., Y. Ikeda, H.K., E.A., H.H., T.F., H.A., J.-i.S., I.K.),

2. Department of Pediatrics (R.I., Y.H.)

3. Department of Cardiac Surgery (K.N., H. Yamauchi, M.O.)

4. Department of Orthopedic Surgery (Y.T.)

5. Department of Advanced Clinical Science and Therapeutics (H.K., J.-i.S.)

6. The University of Tokyo Hospital, Tokyo, Japan. Division of Clinical Pharmacology, Department of Pharmacology (Y. Imai)

7. Division of Cardiovascular Medicine, Department of Internal Medicine (Y. Imai),

8. Jichi Medical University, Shimotsuke, Tochigi, Japan. Jichi Medical University, Shimotsuke, Tochigi, Japan (R.N.).

9. Mitsui Memorial Hospital, Tokyo, Japan (S.T.).

10. Tokyo Teishin Hospital, Tokyo, Japan (Y.H.).

Publisher

Ovid Technologies (Wolters Kluwer Health)

Subject

General Medicine

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