Solitary cutaneous hemorrhagic bullous mastocytoma: A rare entity

Abstract

Solitary cutaneous mastocytoma, a clinical type of cutaneous mastocytosis, may present from birth itself as a macule, plaque, nodule, or bulla. It may be associated with pruritus, flushing attacks, or convulsions. The diagnosis of a solitary mastocytoma is made by the presence of a characteristic skin lesion and confirmed by typical histopathological features of mast cell clusters in dermis and subcutaneous tissues, metachromatic staining of mast cell granules with toluidine blue or giemsa staining, and immunohistochemical mast cell marker c-kit/ CD-117 staining. We report a 4-month-old child who presented with a hemorrhagic bulla of left knee. Skin biopsy and immunohistochemistry confirmed the clinical diagnosis of solitary cutaneous mastocytoma. We did not come across any previous report of solitary cutaneous mastocytoma presenting as hemorrhagic bulla.