Affiliation:
1. Orthopedic Department, Nara Medical University, Nara, Japan
Abstract
Case:
A 46-year-old man with vascular Ehlers-Danlos syndrome (EDS) had an open ankle fracture with a 10 × 5-cm skin defect on the medial side of the ankle. The patient underwent open reduction and internal fixation, as well as coverage of the skin defect with a posterior tibial artery perforator flap, which led to successful outcomes.
Conclusion:
We present the successful implementation of a posterior tibial artery perforator flap for the reconstruction of skin defects in a patient with vascular EDS. Despite the fragility of soft tissues, favorable surgical outcomes were observed.
Publisher
Ovid Technologies (Wolters Kluwer Health)
Subject
Orthopedics and Sports Medicine,Surgery
Reference13 articles.
1. Ehlers-Danlos syndrome in orthopaedics: etiology, diagnosis, and treatment implications;Shirley;Sports Health.,2012
2. The spectrum, management and clinical outcome of Ehlers-Danlos syndrome type IV: a 30-year experience;Oderich;J Vasc Surg.,2005l
3. Characteristics, diagnosis, and management of Ehlers-Danlos syndromes: a review;Joseph;JAMA Facial Plast Surg.,2018
4. The type of variants at the COL3A1 gene associates with the phenotype and severity of vascular Ehlers-Danlos syndrome;Frank;Eur J Hum Genet.,2015
5. Surgical management of vascular Ehlers-Danlos syndrome and its challenges: a case report;da Rocha de Sousa;Swiss Med Wkly.,2020