A young female with hypocomplementemic urticarial vasculitis associated with a rare CNS manifestation-Reference-Cited by-同舟云学术

A young female with hypocomplementemic urticarial vasculitis associated with a rare CNS manifestation

Published:2023-03-01 Issue:2 Volume:20 Page:em459
ISSN:2516-3507
Container-title:Electronic Journal of General Medicine
language:
Short-container-title:ELECTRON J GEN MED

Author:

Alqatari Safi¹^ORCID,Hasan Manal¹^ORCID,Bukhari Raed¹^ORCID,Hadhiah Kawther²^ORCID,Alwaheed Abrar³^ORCID,Alabdrabalnabi Fatimah⁴^ORCID,Al Ohaid Fatimah⁵^ORCID,Aldarwish Abdullah W⁶^ORCID

Affiliation:

1. Internal Medicine and Rheumatology, King Fahad University Hospital, Imam Abdulrahman Bin Faisal University, Dammam, SAUDI ARABIA

2. Neurology, King Fahad University Hospital, Imam Abdulrahman Bin Faisal University, Dammam, SAUDI ARABIA

3. Internal Medicine and Hematology, King Fahad University Hospital, Imam Abdulrahman Bin Faisal University, Dammam, SAUDI ARABIA

4. Internal Medicine, Qatif Central Hospital, Al Qatif, SAUDI ARABIA

5. General Medicine, Saud Al Babtain Cardiac Hospital, Dammam, SAUDI ARABIA

6. King Saud bin Abdulaziz University for Health Sciences, Riyadh, SAUDI ARABIA

Abstract

This case report represents a rare case of 14-year-old female who diagnosed with hypocompementemic urticarial vasculitis syndrome that presents with glomerulonephritis, diffuse alveolar hemorrhage, and acute disseminated encephalomyelitis. The progression of the symptoms explained in the text below in which the final diagnosis was reached after a challenging approach. Patient was managed properly and followed up after treating with rituximab, although she represents no sign of the disease after a total of two cycles.

Publisher

Modestum Ltd

Subject

General Medicine

Link

https://www.ejgm.co.uk/download/a-young-female-with-hypocomplementemic-urticarial-vasculitis-associated-with-a-rare-cns-12859.pdf

Reference19 articles.

1. Jatwani S, Goyal A. Vasculitis. StatPearls. 2022. https://www.ncbi.nlm.nih.gov/books/NBK545186/ (Accessed 1 August 2022).

2. Hoang MP, Park J. Vasculitis. In: Hoang MP, Selim MA, editors. Hospital-based dermatopathology: An illustrated diagnostic guide. Springer International Publishing; 2020. https://doi.org/10.1007/978-3-030-35820-4_7 PMCid:PMC7120156

3. Ion O, Obrișcă B, Ismail G, et al. Kidney involvement in hypocomplementemic urticarial vasculitis syndrome-A case-based review. J Clin Med. 2020;9(7):2131. https://doi.org/10.3390/jcm9072131 PMid:32640739 PMCid:PMC7408727

4. Ueki K, Tsuchimoto A, Matsukuma Y, et al. Hypocomplementemic urticarial vasculitis syndrome with gastrointestinal vasculitis and crescentic membranoproliferative glomerulonephritis without immune complex deposits. CEN Case Rep. 2020;9(1):30-5. https://doi.org/10.1007/s13730-019-00421-4 PMid:31586313 PMCid:PMC6990357

5. Vallianou K, Skalioti C, Liapis G, Boletis JN, Marinaki S. A case report of hypocomplementemicurticarial vasculitis presenting with membranoproliferative glomerulonephritis. BMC Nephrol. 2020;21(1):351. https://doi.org/10.1186/s12882-020-02001-6 PMid:32811472 PMCid:PMC7433181