Affiliation:
1. Amur State Medical Academy
2. Amur Regional Clinical Hospital
Abstract
Aim. The work demonstrates a clinical case of an extremely rare pathology ‒ hemangiomatosis with damage to the skin, subcutaneous tissue, lungs, stomach, intestinal, liver, kidneys, and spine. Results. Patient L., born in 1994 with multiple hemangiomas. No heredity was observed for vascular tumors. In childhood, several large hemangiomas had to be surgically removed. She resorted to the Amur Regional Perinatal Center about her first pregnancy. There was a high risk of hemorrhagic complications due to damage to internal organs, primarily the lungs. Since there were multiple lesions of the vertebrae, it was decided not to use neuraxial methods of anesthesia. Total intravenous anesthesia and artificial ventilation of the lungs under the control of bronchoscopy were chosen by the method of anesthesia. Hemangiomatosis with lesions of internal organs was the indication for a Cesarean section. The operation took place without complications. The child was born healthy. Conclusion. In most cases, cosmetic defects are a significant problem of hemangiomatosis. However, in a number of situations, for example during pregnancy, there is a high risk of rupture of hemangiomas and the development of bleeding. In this case, the choice of the method of delivery and anesthesia depends on the location of the hemangiomas.
Publisher
Far Eastern Scientific Center Of Physiology and Pathology of Respiration
Reference24 articles.
1. ISSVA classification for vascular anomalies. Approved at the 20th ISSVA Workshop. Melbourne, April 2014. Available at: https://www.issva.org/UserFiles/file/Classifications-2014-Final.pdf.
2. Mulliken J.B., Glowacki J. Hemangiomas and vascular malformations in infants and children: a classification based on endothelial characteristics. Plastic and Reconstructive Surgery 1982; 69(3):412–420. Available at: https://www.seman-ticscholar.org/paper/Hemangiomas-and-Vascular-Malformations-in-Infants-A-Mulliken-Glowacki/e188178326227096a68c76d27eb9bccf5cff7abc
3. Okunev N.A., Okuneva A.I., Shchekin O.A., Kalabkin N.A., Budanova M.A. Vascular neoplasms of soft tissues in children: textbook. Saransk; 2019 (in Russian). ISBN 978-5-7103-3780-6
4. Zakharova I.N., Kotlukova N.P., Roginsky V.V., Sokolov J.J., Zaitseva O.V., Maykova I.D., Idrisova G.R., Pshenichnikova I.I. What pediatricians should know about infantile hemangiomas. Meditsinskiy sovet = Medical Council 2016; (16):32–37 (in Russian). https://doi.org/10.21518/2079-701X-2016-16-32-37.
5. Isakov Yu.F., Tikhonov Yu.A. Congenital defects of peripheral vessels in children. Moscow: Meditsina; 1974 (in Russian).