Treatment of an extensive necrotic wound in Weber – Christian – Pfeiffer disease

Abstract

The authors present a successful treatment of a 29-year-old patient with idiopathic Weber – Christian – Pfeiffer panniculitis. after the lumbotomy access for a malignant neoplasm of the right kidney that had provoked the onset of the disease. Edema and hyperemia, aseptic necrotic process at wound edges, hyperthermia, arthralgia, respiratory and cardiovascular insufficiency were initially regarded as a periwound phlegmon and sepsis. In the course of treatment, the diagnosis of idiopathic panniculitis was put pathohistologically. After patient’s stabilization, an extensive wound on the abdominal wall was treated surgically plus physical techniques. A defect in the muscular aponeurotic skeleton of the abdominal wall was replaced with a polypropylene mesh prosthesis. After preparing the wound with negative pressure therapy, the skin grafting was made. Satisfactory immediate and long-term outcomes were achieved.