Two Holes in One: A Rare Case of Congenital Mitral Valve Anomaly

Abstract

Double orifice mitral valve (DOMV) is a rare anomaly, characterised by a mitral valve with a single fibrous annulus resulting in two orifices. Since its discovery in the late 19th century, around 200 cases have been reported. In the Philippines, this mitral valve anomaly has not been reported in literature. The authors are reporting this case to provide information in identifying DOMV using 2D and 3D imaging. The case involves a 26-year-old Filipino man with an incidental finding of an isolated double-orifice mitral valve. Additional imaging using 2D and 3D transoesophageal echocardiography was performed to assess the mitral valve morphology, function and possible associated anomalies. The en face view of the mitral valve showed a complete bridge of tissue extending from the middle of the anterior to the posterior leaflet, creating medial and lateral orifices. The patient presented with an isolated DOMV; hence, no intervention was necessary. However, long-term follow-up is advised.