1. Sinclair and McKay;Rosenthal,1932
2. Hoggins;Rosenthal,1969
3. Case 2. The patient, a 21-year-old male,1952
4. The term aglossia-adactylia is misleading. Aglossia indicates total absence of the tongue which is rarely the case. Although a few cases have had an 'almost' total absence of the tongue;Fulford, Ardran; Kemp, 1956, Nevin,1932
5. The limb anomalies are also extremely variable. Any limb may be involved and variability of the limb anomalies may be observed in the same individual as well as in different patients. In general, the anomalies of the upper limbs tend to be distal to the humerus; those of the lower limb distal to the femur. Hemimelia of the upper limbs and minor anomalies of the feet have been reported in the same patient (Gorlin and Pindborg, 1964; Cohen et al;Nevin et al,1971