Abstract
Abstract
Background
Cholesteatoma is regarded as a critical health issue in the world. Nevertheless, congenital cholesteatoma (CC) is an unusual problem, and bilateral CC is extremely rare.
Case presentation
The present work reports a young boy with conductive hearing loss because of CC. The left side was operated using a canal-wall-down mastoidectomy method for immense destruction of the middle ear structures and mastoid air cells, and endoscopic ear surgery was performed on the second side.
Conclusion
Although CC is very rare, it should be considered in the differential diagnosis of hearing loss in children. Moreover, it should be carefully followed up because it can probably occur on the second side.
Publisher
Springer Science and Business Media LLC
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