Author:
Lele Mutombo Fabrice,Nzanzu Kikuhe Jason,Kasereka Mwanamolo Noé,Erickson Marc H.,Wetzig Neil,Kabuyaya Kakule Médard
Abstract
Abstract
Background
Epignathus is a rare, benign, congenital teratoma of the hard palate with an estimated incidence of 1 in 200,000 live births. Epignathus frequently leads to a high mortality (80–100%) due to airway obstruction in the neonatal period.
Case presentation
We report a case of successful management of a rare oropharyngeal teratoma in a African newborn girl who was referred to our institute with a large protruding intraoral mass, combined with cleft palate, causing some respiratory compromise. The palatal mass was removed on the fifth day after birth, and a palatoplasty performed on day 30.
Conclusion
Epignathus is a life-threatening condition at the time of delivery. Appropriate management begins with securing the airway, followed by complete resection of the tumor.
Publisher
Springer Science and Business Media LLC
Reference13 articles.
1. Omezzine M, Bouslama S, Nouri S, Moatamri R, Khochtali H. Tumeurs congénitales de la cavité buccale et fente palatine: présentation de 2 cas. Med Buccale Chir Buccale. 2011;17(2):167–9. https://doi.org/10.1051/mbcb/2011109.
2. Kundal V, Gajdhar M, Sharma C, Kundal R. Intraoral teratoma in a newborn presenting as severe respiratory distress. BMJ Case Rep. 2013;2013(251):2013008735–2013008735.
3. Meziane M, Eabdenbitsen A, Boulaadas M, Essakalli L, Kzadri M. Double tératome de la cavité buccale? Med Buccale Chir Buccale. 2012;18(4):383–5. https://doi.org/10.1051/mbcb/2012039.
4. Al-Mahdi A, Al-Khurrhi LE, Atto GZ, Dhaher A. Giant epignathus teratoma involving the palate, tongue, and floor of the mouth. J Craniofac Surg. 2013;24(1):e97–9.
5. Menezes Filho MP, Simao NMMS. Giant epignathus of the palate: a case report. J Bras Patol Med Lab. 2015. https://doi.org/10.5935/1676-2444.20150055.
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