Author:
Guelngar Carlos Othon,Mohamed Lamine Touré,Mamadou Ciré Barry,Mamady Diakité,Mahadi Konaté,Bachir Abdoul Djibo Hamani,Foksouna Sakadi,Fatimata Djibo Hassane,Naby Camara,Dago François Kassa,Fatimatou Korka Bah,Doussou Camara,Victorine Millimono,Salematou Condé,Aminata Sakho,Mohamed Tafsir Diallo,Souleymane Djigué Barry,Mamadou Saliou Diallo,Fodé Mohamed Soumah,Aminou Sanni Yaya,Daouya Douna Granga,Said Abdallah Rafkat,Mamady Konaté,Souleymane Mbara Diallo,Fodé Abass Cissé,Amara Cissé
Abstract
Abstract
Background
In sub-Saharan Africa, encephalitis of various etiologies is a major public health problem and Rasmussen syndrome is rarely diagnosed due to under-medicalization. The objective of this study is to describe the clinical and neuroradiological forms, especially since this affection is little known in sub-Saharan Africa as evidenced by the scarcity of publications.
Results
A retrospective, descriptive and analytical study of six (6) cases of Rasmussen syndrome, shows that it is an unrecognized disease in Africa. Men were more represented with a frequency of 67% with a young age. The clinical picture dominated by 100% seizures, mental deterioration and hemiparesis. The etiology is still questionable, probably autoimmune in our study.
Conclusion
Rasmussen syndrome accounts for 3% in 219 patients hospitalized for epileptic conditions. This study shows a clinical profile dominated by recurrent epileptic seizures refractory to the drugs Phenobarbital, Valproic Acid and Carbamazepine, the only antiepileptics available in the country. These results are valid for therapeutic and prognostic discussion.
Publisher
Springer Science and Business Media LLC
Subject
Psychiatry and Mental health,Clinical Neurology,General Neuroscience,Phychiatric Mental Health,Surgery
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