Author:
Ji Yi,Xu Bing,Wang Xuejun,Liu Wenying,Chen Siyuan
Abstract
Abstract
Plexiform neurofibromas are benign tumors originating from subcutaneous or visceral peripheral nerves, which are usually associated with neurofibromatosis type 1. They are almost always congenital lesions and often cause the surrounding soft tissue and bone to grow aberrantly. We treated a 12-year-old boy who presented with asymmetric pectus excavaum and an anterior chest wall plexiform neurofibroma. The pectus excavaum was corrected by modified Nuss procedure, followed by simultaneous resection of the giant mass. The patient is doing well at the 4 years follow-up visit.
Publisher
Springer Science and Business Media LLC
Subject
Cardiology and Cardiovascular Medicine,General Medicine,Surgery,Pulmonary and Respiratory Medicine
Reference17 articles.
1. Nguyen R, Kluwe L, Fuensterer C, Kentsch M, Friedrich RE, Mautner VF: Plexiform Neurofibromas in Children with Neurofibromatosis Type 1: Frequency and Associated Clinical Deficits. J Pediatr. 2011
2. Korf BR: Malignancy in neurofibromatosis type 1. Oncologist. 2000, 5 (6): 477-485. 10.1634/theoncologist.5-6-477.
3. Gutmann DH, Aylsworth A, Carey JC, Korf B, Marks J, Pyeritz RE, Rubenstein A, Viskochil D: The diagnostic evaluation and multidisciplinary management of neurofibromatosis 1 and neurofibromatosis 2. JAMA. 1997, 278 (1): 51-57. 10.1001/jama.278.1.51.
4. Fois A, Calistri L, Balestri P, Vivarelli R, Bartalini G, Mancini L, Berardi A, Vanni M: Relationship between cafe-au-lait spots as the only symptom and peripheral neurofibromatosis (NF1): a follow-up study. Eur J Pediatr. 1993, 152 (6): 500-504. 10.1007/BF01955059.
5. Akcali Y, Ceyran H, Hasdiraz L: Chest wall deformities. Acta Chir Hung. 1999, 38 (1): 1-3.
Cited by
8 articles.
订阅此论文施引文献
订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献