Abstract
Abstract
Background
Pulmonary hypertension (PH) is commonly seen in adults who have congenital heart disease (CHD). Therapy is available for pulmonary arterial hypertension (PAH) and has greatly benefitted many patients with PAH related to CHD (PAH-CHD) over the last 15 years, with evidence of improved quality of life and prognosis in those with Eisenmenger syndrome and repaired PAH-CHD.
In this review, we describe the standard management and advanced therapies for PAH, which are available in specialist PH centres around the UK and Ireland, and how these are used in PAH-CHD. Decisions around the choice of therapy are governed by commissioning and available evidence.
Conclusion
We explain the different pathways for action and the variety of medications now at our disposal to help this important group of patients.
Publisher
Springer Science and Business Media LLC
Subject
Management Science and Operations Research,Mechanical Engineering,Energy Engineering and Power Technology
Cited by
5 articles.
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