Comprehensive study into the activation of the plasma enzyme systems during attacks of hereditary angioedema due to C1-inhibitor deficiency

Author:

Csuka Dorottya,Veszeli Nóra,Imreh Éva,Zotter Zsuzsanna,Skopál Judit,Prohászka Zoltán,Varga Lilian,Farkas Henriette

Publisher

Springer Science and Business Media LLC

Subject

Pharmacology (medical),Genetics(clinical),General Medicine

Reference38 articles.

1. Zeerleder S. C1-inhibitor: more than a serine protease inhibitor. Semin Thromb Hemost. 2011;37(4):362–74. doi: 10.1055/s-0031-1276585 .

2. Forbes CD, Pensky J, Ratnoff OD. Inhibition of activated Hageman factor and activated plasma thromboplastin antecedent by purified serum C1 inactivator. J Lab Clin Med. 1970;76(5):809–15.

3. van der Graaf F, Keus JF, Koedam JA, Rietveld A, Bouma BN. Prekallikrein activation and kallikrein inactivation in human plasma. Adv Exp Med Biol. 1983;156:143–8.

4. Wuillemin WA, Minnema M, Meijers JC, Roem D, Eerenberg AJ, Nuijens JH, et al. Inactivation of factor XIa in human plasma assessed by measuring factor XIa-protease inhibitor complexes: major role for C1-inhibitor. Blood. 1995;85(6):1517–26.

5. Pixley RA, Schapira M, Colman RW. The regulation of human factor XIIa by plasma proteinase inhibitors. J Biol Chem. 1985;260(3):1723–9.

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