Agenesis of the Hepatic Vena Cava in a Patient with Scimitar Syndrome

Abstract

With the use of sophisticated imaging modalities, congenital anomalies of the inferior vena cava and its tributaries, such as agenesis of the hepatic vena cava, are becoming more and more commonly encountered. Scimitar syndrome, also called venolobar syndrome and hypogenetic lung syndrome, is a rare pulmonary vascular anomaly of the right lung that can sometimes be associated with some cardiovascular anomalies. We present here a case with agenesis of the hepatic vena cava associated with scimitar syndrome.