Stoma takedown after Hartmann’s procedure in a patient with hemophilia A complicated with production of inhibitor to FVIII (review and case report)-Reference-Cited by-同舟云学术

Stoma takedown after Hartmann’s procedure in a patient with hemophilia A complicated with production of inhibitor to FVIII (review and case report)

Published:2022-12-21 Issue:4 Volume:21 Page:130-138
ISSN:2686-7303
Container-title:Koloproktologia
language:
Short-container-title:Koloproktologiâ

Author:

Shtyrkova S. V.¹^ORCID,Shutov S. A.¹^ORCID,Batrov P. A.¹^ORCID,Rybakov E. G.²^ORCID,Prasolov N. V.¹^ORCID

Affiliation:

1. National Medical Research Center for Hematology

2. National Medical Research Center of Coloproctology

Abstract

One of the specific manifestations of hemophilia A is the spontaneous abdominal hematoma mimicking the clinical picture of acute abdominal disease. The appearance of auto-antibodies to FVIII leads to a loss of response to replacement hemostatic therapy and requires an individualized approach as well as highly sensitive laboratory monitoring to reduce the risk of uncontrolled bleeding. The paper presents the case of multi-stage surgical treatment of this complication.

Publisher

Russian Association of Coloproctology

Subject

Gastroenterology,Oncology,Surgery

Reference18 articles.

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