Aberrant long-chain fatty acid metabolism associated with evolving systemic sclerosis-associated pulmonary arterial hypertension-Reference-Cited by-同舟云学术

Aberrant long-chain fatty acid metabolism associated with evolving systemic sclerosis-associated pulmonary arterial hypertension

Published:2024-07-01 Issue:1 Volume:327 Page:L54-L64
ISSN:1040-0605
Container-title:American Journal of Physiology-Lung Cellular and Molecular Physiology
language:en
Short-container-title:American Journal of Physiology-Lung Cellular and Molecular Physiology

Author:

Coursen Julie C.¹^ORCID,Tuhy Tijana²,Naranjo Mario³^ORCID,Woods Adrianne⁴,Hummers Laura K.⁴,Shah Ami A.⁴,Suresh Karthik²^ORCID,Visovatti Scott H.⁵,Mathai Stephen C.²,Hassoun Paul M.²^ORCID,Damico Rachel L.²,Simpson Catherine E.²^ORCID

Affiliation:

1. Division of Hospital Medicine, Department of Medicine, Johns Hopkins University, Baltimore, Maryland, United States

2. Division of Pulmonary and Critical Care Medicine, Department of Medicine, Johns Hopkins University, Baltimore, Maryland, United States

3. Department of Thoracic Medicine and Surgery, Temple University, Philadelphia, Pennsylvania, United States

4. Division of Rheumatology, Department of Medicine, Johns Hopkins University, Baltimore, Maryland, United States

5. Division of Cardiology, Department of Medicine, The Ohio State University, Columbus, Ohio, United States

Abstract

Abnormal lipid metabolism is evident across time in the development of SSc-PAH, and dysregulated long-chain fatty acid metabolism predicts overt PAH.

Funder

Johns Hopkins inHealth

Donald B. and Dorothy L. Stabler Foundation

Nancy and Joachim Bechtle Precision Medicine Fund for Scleroderma

Sara and Alex Othon Fund

Manugian Family Scholar

HHS | NIH | National Institute of Arthritis and Musculoskeletal and Skin Diseases

HHS | National Institutes of Health

National Scleroderma Foundation

Pulmonary Hypertension Association

U.S. Department of Defense

Publisher

American Physiological Society

Link

https://journals.physiology.org/doi/pdf/10.1152/ajplung.00057.2024

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