2020 Chinese expert-based consensus on the diagnosis and treatment of connective tissue disease associated pulmonary arterial hypertension-Reference-Cited by-同舟云学术

2020 Chinese expert-based consensus on the diagnosis and treatment of connective tissue disease associated pulmonary arterial hypertension

Published:2021-06-01 Issue:2 Volume:2 Page:63-78
ISSN:2719-4523
Container-title:Rheumatology and Immunology Research
language:en
Short-container-title:

Author:

Zhao Jiuliang¹,Wang Qian¹,Wang Qiang²,Zhang Yongfeng³,Zhang Na⁴,Zhang Rong⁵,Hao Yanjie⁶,Jia Junfeng⁷,Li Mengtao¹,Zeng Xiaofeng¹

Affiliation:

1. Department of Rheumatology, Peking Union Medical College Hospital (PUMCH), Chinese Academy of Medical Sciences, National Clinical Research Center for Dermatologic and Immunologic Diseases (NCRC-DID), Key Laboratory of Rheumatology and Clinical Immunology, Ministry of Education, Chinese Rheumatism Data Center (CRDC), Chinese SLE Treatment and Research Group (CSTAR) , Beijing , China

2. Department of Rheumatology , The First Affiliated Hospital of Nanjing Medical University , Nanjing , Jiangsu Province , China

3. Department of Rheumatology, Beijing Chaoyang Hospital , Capital Medical University , Beijing , China

4. Department of Rheumatology , Tianjin Medical University General Hospital , Tianjin , China

5. Department of Rheumatology , The First Affiliated Hospital of China Medical University , Shenyang , Liaoning Province , China

6. Department of Rheumatology and Clinical Immunology , Peking University First Hospital , Beijing , China

7. Department of Clinical Immunology, PLA Specialised Research Institute of Rheumatology and Immunology, Xijing Hospital , Fourth Military Medical University , Xi’an , Shaanxi Province , China

Abstract

Abstract Pulmonary arterial hypertension (PAH) is a severe complication of connective tissue disease (CTD) and is one of the leading causes of morbidity and mortality among patients with this condition. To establish an expert-based consensus on the diagnosis and treatment of CTD-associated PAH, a multidisciplinary consensus development panel was established. The consensus panel is composed of 45 experts in rheumatology, cardiology, pulmonology, and radiology, most of whom are members of the Group of Pulmonary Vascular and Interstitial Lung Diseases (ILD) Associated with Rheumatic Diseases. The consensus development panel compiled 9 recommendations for the diagnosis and treatment of CTD-associated PAH. It covers screening, diagnosis, disease evaluation, risk assessment, the use of immunosuppressive agents, and PAH-specific therapy with a treat-to-target approach. The consensus is intended to facilitate decision-making and standardize the care of CTD-associated PAH in China.

Publisher

Walter de Gruyter GmbH

Link

https://www.degruyter.com/document/doi/10.2478/rir-2021-0010/pdf

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