Leiomyosarcoma of inferior vena cava complicated by Budd-Chiari syndrome and disseminated intravascular coagulation — case report

Author:

Krakowska-Stasiak Małgorzata1,Kosałka Joanna2,Wójcik Krzysztof2,Sokołowska Barbara2,Szpor Joanna3,Grys Iwon1,Musiał Jacek2

Affiliation:

1. 1Department of Internal Medicine and Gastroenterology, 5th Military Clinical Hospital in Kraków, Wrocławska Street 1-3, 30-901, Kraków, Poland

2. 22nd Department of Internal Medicine, Unit of Allergy and Clinical Immunology, Medical College, Jagiellonian University, Kraków, Poland

3. 3Department of Pathomorphology, Medical College, Jagiellonian University, Kraków, Poland

Abstract

AbstractLeiomyosarcoma of inferior vena cava is a rare malignant mesenchymal tumor of the venous system that typically occurs in adulthood. Correct and early recognition of leiomyosarcoma is very important, because a complete resection of the tumor (with occasionally chemio-or radiotherapy) can lead to prolonged survival. We report a case of a 54-year-old man suffering from the leiomyosarcoma of inferior vena cava with infiltration of retroperitoneum and right adrenal gland.

Publisher

Walter de Gruyter GmbH

Subject

General Medicine

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