Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus-Reference-Cited by-同舟云学术

Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus

Published:2022-12-01 Issue:3 Volume:22 Page:122-128
ISSN:1338-4139
Container-title:Acta Medica Martiniana
language:en
Short-container-title:

Author:

Jakub Hoferica¹,Lenka Nosakova¹,Peter Uhrik¹,Diana Vazanova¹,Matus Scur¹,Juraj Chudej²,Peter Banovcin¹

Affiliation:

1. Clinic of Gastroenterological Internal Medicine, University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava , Martin , Slovakia

2. Department of Hematology and Transfusiology of University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava , Martin , Slovakia

Abstract

Abstract In this work we describe a rare case of a patient with paroxysmal nocturnal hemoglobinuria (PNH) developed on the background of specific medical history of morbus Gilbert with chronically elevated bilirubin and recurrent attacks of macroscopic haematuria. We focus on a differential diagnosis of the disease, its obstacles, and treatment options.

Publisher

Walter de Gruyter GmbH

Subject

General Biochemistry, Genetics and Molecular Biology,General Nursing

Link

https://www.sciendo.com/pdf/10.2478/acm-2022-0014

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