A Case of Hepatosplenic γ/δ T-Cell Lymphoma Debuting With Massive Hemoptysis-Reference-Cited by-同舟云学术

A Case of Hepatosplenic γ/δ T-Cell Lymphoma Debuting With Massive Hemoptysis

Published:2023-06-01 Issue:1 Volume:16 Page:58-61
ISSN:1313-9053
Container-title:Journal of Biomedical and Clinical Research
language:en
Short-container-title:

Author:

Antonov Antonio I.¹

Affiliation:

1. 1 Department of Clinical Hematology, Medical University – Varna, St. Marina University Hospital , Varna , Bulgaria , St. Marina, University Hospital , Pleven , Bulgaria , Department of Clinical Hematology

Abstract

Summary Hepatosplenic γ/δ T-cell lymphoma (HSTL) is a very rare, aggressive extranodal lymphoma affecting mainly young adults. Clinically, presents with a symptomatic hepatosplenomegaly and systemic symptoms but without lymphadenopathy. The diagnosis is confirmed after careful evaluation of bone marrow and liver biopsies or, in some cases, after diagnostic splenectomy. Overall, survival is short regardless of chemotherapy regimens applied, including autologous stem cell transplantation. We present a case of γ/δ HSTL with massive pulmonary hemoptysis requiring bronchial artery embolization.

Publisher

Walter de Gruyter GmbH

Subject

General Medicine

Link

https://www.sciendo.com/pdf/10.2478/jbcr-2023-0008

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