A case of genetic Creutzfeldt–Jakob disease that required differential diagnosis of acute encephalopathy associated with Sjogren’s syndrome
Author:
Affiliation:
1. Department of Neurology and Stroke Treatment, Kyoto First Red Cross Hospital
2. Department of Neurology, Omihachiman Community Medical Center
Publisher
Societas Neurologica Japonica
Subject
Neurology (clinical)
Link
https://www.jstage.jst.go.jp/article/clinicalneurol/62/3/62_cn-001672/_pdf
Reference17 articles.
1. 1) Rabinovici GD, Wang PN, Levin J, et al. First symptom in sporadic Creutzfeldt-Jakob disease. Neurology 2006;66:286-287.
2. 2) Shiga Y, Miyasawa K, Sato S, et al. Diffusion-weighted MRI abnormalities as an early diagnostic marker for Creutzfeldt-Jakob disease. Neurology 2004;63:443-449.
3. 3) Chitravas N, Jung RS, Kofskey DM, et al. Treatable neurological disorders misdiagnosed as Creutzfeldt-Jakob disease. Ann Neurol 2011;70:437-444.
4. 4) Matsuo K, Saburi M, Ishikawa H, et al. Sjögren syndrome presenting with encephalopathy mimicking Creutzfeldt-Jakob disease. J Neurol Sci 2013;326:100-103.
5. 5) 徳田直輝,今井啓輔,笠井高士ら.ステロイド・パルス療法,血漿交換療法,免疫グロブリン静注療法に抵抗性で,長期ステロイド経口投与が有効であった橋本脳症の1例.臨床神経 2015;55:737-774.
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