Ketogenic therapy in childhood and adolescence: recommendations of the Brazilian experts group

Author:

de Brito Sampaio Letícia Pereira1ORCID,Henriques-Souza Adélia Maria de Miranda2ORCID,Lin Katia3ORCID,Neri Lenycia de Cassya Lopes1ORCID,Inuzuka Luciana Midori4ORCID,Uchôa Ludmila Inácio de Lima5ORCID,Gregório Marcela Marques de Oliveira6ORCID,Guilhoto Laura Maria67ORCID,Montenegro Maria Augusta8ORCID,Lunardi Mariana9ORCID,Veiga Marielza10ORCID,de Lima Patricia Azevedo11ORCID,Braatz Vera12ORCID

Affiliation:

1. Universidade de São Paulo, Faculdade de Medicina, Hospital das Clínicas, Instituto da Criança e Adolescente, São Paulo SP, Brazil.

2. Instituto de Medicina Integral Professor Fernando Figueira, Centro de Terapias Cetogênicas do IMIP, Recife PE, Brazil.

3. Universidade Federal de Santa Catarina, Departamento de Medicina Interna, Divisão de Neurologia, Florianópolis SC, Brazil.

4. Hospital Sirio Libanês, Departamento de Neurofisiologia, São Paulo SP, Brazil.

5. Hospital Materno-Infantil de Brasília, Brasília DF, Brazil.

6. Universidade Federal de São Paulo, Departamento de Neurologia, São Paulo, Brazil.

7. Universidade de São Paulo, Hospital Universitário, Divisão de Clínica Pediátrica, São Paulo SP, Brazil.

8. Universidade Estadual de Campinas, Departamento de Neurologia, São Paulo SP, Brazil.

9. Universidade Federal de Santa Catarina, Programa de Pós-Graduação em Ciências Médicas, Florianópolis SC, Brazil.

10. Hospital Universitário Professor Edgard Santos, Salvador BA, Brazil.

11. Universidade Anhanguera, São Paulo SP, Brazil.

12. Universidade da Região de Joinville, Departamento de Medicina, Divisão de Neurologia, Joinville SC, Brazil.

Abstract

AbstractKetogenic dietary therapies (KDTs) are a safe and effective treatment for pharmacoresistant epilepsy in children. There are four principal types of KDTs: the classic KD, the modified Atkins diet (MAD), the medium-chain triglyceride (MCT) diet, and the low glycemic index diet (LGID). The International Ketogenic Diet Study Group recommends managing KDTs in children with epilepsy. However, there are no guidelines that address the specific needs of the Brazilian population. Thus, the Brazilian Child Neurology Association elaborated on these recommendations with the goal of stimulating and expanding the use of the KD in Brazil.

Publisher

Georg Thieme Verlag KG

Subject

Neurology,Neurology (clinical)

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