Case Report of Undifferentiated Hepatic Embryonal Sarcoma with Mesenchymal Hamartoma: A Rare Entity-Reference-Cited by-同舟云学术

Case Report of Undifferentiated Hepatic Embryonal Sarcoma with Mesenchymal Hamartoma: A Rare Entity

Published:2022-12-09 Issue:01 Volume:06 Page:071-076
ISSN:2581-9178
Container-title:Journal of Gastrointestinal and Abdominal Radiology
language:en
Short-container-title:Journal of Gastrointestinal and Abdominal Radiology

Author:

Jacob Dhanya¹,Pratap Thara¹,Yadav Abhishek²,Jalal Muhammed Jasim Abdul³,Mahadevan Pushpa⁴,Unnikrishnan Reshmi⁵

Affiliation:

1. Department of Radiology, VPS Lakeshore Hospital, Kochi, Kerala, India

2. Department of Comprehensive Liver Care, VPS Lakeshore Hospital, Kochi, Kerala, India

3. Department of Internal Medicine and Rheumatology, VPS Olive Healthcare, Thrissur, Kerala, India

4. Department of Pathology, VPS Lakeshore Hospital, Kochi, Kerala, India

5. Department of Paediatrics, VPS Lakeshore Hospital, Kochi, Kerala, India

Abstract

AbstractUndifferentiated embryonal sarcoma (UES) is a highly malignant hepatic neoplasm, which occurs mostly in pediatric population. There is a link between embryonal sarcoma and mesenchymal hamartoma as evidenced by clinicopathological overlap and similar genetic abnormality. Here, we report a case of UES in a young female in a background of mesenchymal hamartoma of liver.

Publisher

Georg Thieme Verlag KG

Subject

General Medicine,General Chemistry

Link

http://www.thieme-connect.de/products/ejournals/pdf/10.1055/s-0042-1758125.pdf

Reference16 articles.

1. Characteristics and outcomes in children with undifferentiated embryonal sarcoma of the liver: a report from the National Cancer Database;Y Shi;Pediatr Blood Cancer,2017

2. Undifferentiated embryonal sarcoma with unusual features arising within mesenchymal hamartoma of the liver: report of a case and review of the literature;M J O'Sullivan;Pediatr Dev Pathol,2001

3. Undifferentiated embryonal sarcoma of the liver in adults;F Lenze;Cancer,2008

4. Long-term survival outcomes of undifferentiated embryonal sarcoma of the liver: a pooled analysis of 308 patients;Z Wu;ANZ J Surg,2020

5. Primary hepatic tumors of childhood;A G Weinberg;Hum Pathol,1983