Affiliation:
1. Paramedic, London Ambulance Service NHS Trust, London, UK
Abstract
Sickle cell disease (SCD) covers a group of inherited conditions that affect the red blood cells. It can cause episodes of intense pain called sickle cell crises. This case study outlines a 10-year-old boy's first presentation of sickle cell crisis. The patient presents with typical sickle cell crisis pain in joints that is exacerbated by movement and related to strenuous physical exercise in the cold. This pain is caused by the sickled red blood cells occluding the microvasculature, causing tissue ischaemia. SCD is a serious disease and requires early recognition through robust clinical assessment to reduce the potential for fatality, complications and morbidity. Understanding the pathology of disease ensures paramedics work appropriately, using their knowledge to identify a patient with SCD and using skills to inform practice. Initiating the correct treatment is paramount in reducing the likelihood of fatal complications.
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