Hydroa vacciniforme-like lymphoma: a chronic EBV+ lymphoproliferative disorder with risk to develop a systemic lymphoma

Author:

Quintanilla-Martinez Leticia1,Ridaura Cecilia2,Nagl Florian1,Sáez-de-Ocariz Marimar3,Durán-McKinster Carola3,Ruiz-Maldonado Ramon3,Alderete Georgia2,Grube Peter2,Lome-Maldonado Carmen4,Bonzheim Irina1,Fend Falko1

Affiliation:

1. Institute of Pathology and Comprehensive Cancer Center, Eberhard-Karls-University of Tübingen, Tübingen, Germany;

2. Pathology and

3. Dermatology Departments, Instituto Nacional de Pediatria, Mexico City, Mexico; and

4. Pathology Department, Instituto Nacional de Ciencias Medicas y Nutrición, Salvador Zubirán, Mexico City, Mexico

Abstract

Key Points HVLL is a chronic EBV+ lymphoproliferative disorder of childhood with risk to develop systemic lymphoma. The disease shows favorable response to conservative therapy despite the presence of a T- or NK-cell monoclonal proliferation.

Publisher

American Society of Hematology

Subject

Cell Biology,Hematology,Immunology,Biochemistry

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