Hereditary Hemolytic Anemia Associated With Abnormal Membrane Lipid. II. Ion Permeability and Transport Abnormalities-Reference-Cited by-同舟云学术

Hereditary Hemolytic Anemia Associated With Abnormal Membrane Lipid. II. Ion Permeability and Transport Abnormalities

Published:1973-07-01 Issue:1 Volume:42 Page:1-8
ISSN:0006-4971
Container-title:Blood
language:en
Short-container-title:

Author:

Shohet Stephen B.¹²,Nathan David G.¹³,Livermore Barbara M.¹⁴,Feig Stephen A.¹⁵,Jaffé Ernst R.¹⁶

Affiliation:

1. Division of Hematology, Department of Medicine, the Children’s Hospital Medical Center, the Department of Pediatrics, Harvard Medical School, Boston, Mass. 02115; and the Department of Medicine, Albert Einstein College of Medicine, Bronx, N. Y. 10461.

2. Hematology Laboratories, University of California Medical Center, San Francisco, Calif. 94122; Recipient of USPHS Career Development Award AM 37237.

3. Harvard Medical School, Boston, Mass. 02115; Recipient of USPHS Career Development Award AM 35361-05.

4. Woman's Medical College, Philadelphia, Pa. 19129.

5. Division of Hematology, University of California School of Medicine, Los Angeles, Calif. 90024.

6. Acting Dean Albert Einstein College of Medicine of Yeshiva University, Bronx, N. Y. 10461.

Abstract

Abstract A familial nonspherocytic hemolytic anemia with altered red cell membrane lipids has been described. The membrane lipid lesion is also accompanied by excessive cation permeability and ouabain-sensitive pumping, which is in turn associated with excessive glycolytic energy diverted to the pump. This permeability defect and its demands for glycolytic energy are thought to contribute significantly to the early demise of the red cell in this disorder.

Publisher

American Society of Hematology

Subject

Cell Biology,Hematology,Immunology,Biochemistry

Link

http://ashpublications.org/blood/article-pdf/42/1/1/577747/1.pdf

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