Kinetic results for mutations of conserved residues H304 and R309 of human sulfite oxidase point to mechanistic complexities-Reference-Cited by-同舟云学术

Kinetic results for mutations of conserved residues H304 and R309 of human sulfite oxidase point to mechanistic complexities

Published:2014 Issue:9 Volume:6 Page:1664-1670
ISSN:1756-5901
Container-title:Metallomics
language:en
Short-container-title:Metallomics

Author:

Davis Amanda C.¹²³,Johnson-Winters Kayunta¹⁴⁵,Arnold Anna R.¹²³,Tollin Gordon¹²³,Enemark John H.¹²³

Affiliation:

1. Department of Chemistry and Biochemistry

2. University of Arizona

3. Tucson, USA

4. University of Texas at Arlington

5. Arlington, USA

Abstract

Several point mutations in the gene of human sulfite oxidase (hSO) result in isolated sulfite oxidase deficiency, an inherited metabolic disorder.

Publisher

Oxford University Press (OUP)

Subject

Metals and Alloys,Biochemistry,Biomaterials,Biophysics,Chemistry (miscellaneous)

Link

http://pubs.rsc.org/en/content/articlepdf/2014/MT/C4MT00099D

Reference42 articles.

1. K. V. Rajagopalan , Sulfite Oxidase (Sulfite:Ferricytochrome c Oxidoreductase) , in Molybdenum and Molybdenum-Containing Enzymes , ed. M. P. Coughlan , Pergamon Press , Oxford, U.K. , 1st edn, 1980 , pp. 241–272

2. The reaction mechanism of oxomolybdenum enzymes

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