Affiliation:
1. Krasnoyarsk State Medical University named after Professor V. F. Voyno-Yasenetsky
2. Krasnoyarsk State Medical University named after Professor V. F. Voyno-Yasenetsky
3. Clinical Hospital named after I.S. Berzon
4. Krasnoyarsk Clinical Hospital named after I.S. Berzon
Abstract
The article provides an observation of the clinical detection of familial hereditary hemorrhagic
telangiectasia (Osler-Weber-Rondu disease), which is manifested by a tumor of the transformation of small
foci in multiple telangiectasias, on the skin, mucous and serous membranes, arteriovenous shunts in the internal
organs and aneurysms, which is manifested by bleeding. This rare defect had various clinical manifestations
in the mother and caused relapses of pulmonary circulation in the child and, as a result, posthemorrhagic ane mia. The given obligatory observation by a pediatrician should be directed to severe symptoms of the disease
and obligatory compliance with the requirements and treatment
Publisher
Astrakhan State Medical University
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