Affiliation:
1. National Medical Research Center for Otorhinolaryngology of the Federal Medico-Biological Agency of Russia
Abstract
Endolymphatic sac tumors are rare neoplasms of the temporal bone, histologically benign, but clinically behaves as malignant tumors causing destruction of surrounding tissues. The tumor originates from the posterior surface of petrous part of temporal bone, where endolymphatic sac is situated anatomically. The tumor causes destruction of the posterior surface of the petrous part of the temporal bone, inner ear, mastoid process, etc. Endolymphatic sac tumor can be both sporadically and in patients with von Hippel – Lindau disease. Due to the rarity of this tumor, it is easy to confuse it with other tumors, such as paraganglioma, middle ear adenoma, adenocarcinoma, papillary thyroid carcinoma or papilloma of the vascular plexus. Computed tomography (CT) and magnetic resonance imaging (MRI) are of great diagnostic importance and play an important role in planning treatment tactics. The optimal method of treatment is resection of pathologically altered tissues. In some cases (incomplete resection of tumor, the patients with concomitant diseases or inoperable cases) receive courses of X-ray or radiosurgery. If a tumor is detected in the early stages, the volume of resection can be minimized while preserving hearing and vestibular function of the inner ear. Recurrence usually happens due to difficulty to identify the extension of the tumor. Diagnosis and correct preoperative planning, with embolization if it possible, will facilitate surgery and avoid subtotal tumor resection due to intraoperative bleeding. Long follow-up period is important in order to avoid recurrences. Insufficient coverage of this problem in the literature is associated with a low percentage of its occurrence in otosurgical practice, which complicates the timely diagnosis and treatment of this type of tumors of the temporal bone, worsens the prognosis.
Reference100 articles.
1. Kumar M., Ramakrishnaiah R., Muhhamad Y., Hemert R., Angtuaco E. Endolymphatic sac tumor. Radiol Case Rep. 2011;6(3):372. https://doi.org/10.2484/rcr.v6i3.372.
2. Liu Y., Xie J., Ge X, Gong S. Endolymphatic sac tumor with symptoms of endolymphatic hydrops: a case report and reviews. Lin Chung Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2020;34(5):468–469. (In Chinese). https://doi.org/10.13201/j.issn.2096-7993.2020.05.021.
3. Michaels L. Origin of endolymphatic sac tumor. Head Neck Pathol. 2007;1:104–111. https://doi.org/10.1007/s12105-007-0016-3.
4. Czopek J., Wasko M., Adamek D. Endolymphatic sac tumor, case report of a rare tumor of the temporal bone presenting as a mass in cerebello-p ontine angle. Folia Neuropathol. 2013;51(2):164–168. https://doi.org/10.5114/fn.2013.35960.
5. Banerjee A., Whyte A., O’Sullivan P. Atlas Endolymphatic sac tumor. Otol Neurotol. 2005;26(4):819–820. https://doi.org/10.1097/01.mao.0000178143.06387.44.
Cited by
1 articles.
订阅此论文施引文献
订阅此论文施引文献,注册后可以免费订阅5篇论文的施引文献,订阅后可以查看论文全部施引文献