A Case Report On Prune Belly Syndrome

Abstract

Eagle-Barrett syndrome’ is the other name for prune belly syndrome. The classical triad of urinary tract anomalies,deficient abdominal musculature, and bilateral cryptorchidism. It is a congenital anomaly of unknown aetiology, most commonlyseen in males. It is seen in one and 30,000 live births.96% of them are males. In this case report, we present a boy child born toA 38-year-old multigravida mother with a previous history of three vaginal deliveries. On examination of the baby, the followingfeatures are to be found-hypotonia, deficiency of abdominal muscle, undescended testis, a palpable bladder and kidney. Radiologicalimaging showed gross hydronephrosis on both sides and big ureter. The baby was diagnosed with Prune Belly syndrome.Ultrasound investigations done during the antenatal period, helps in directing anomalies of the kidney which is to be followed inthe postnatal period. The aim of the writing this case report is to establish the importance of antenatal diagnosis of congenitalmalformations including Eagle-Barrett Syndrome among many others. Prenatal diagnosis of PBS should be considered wheneverthe following ultra- sound anomalies are clearly identified: oligohydramnios, urinary abnormalities (dilatation of the urinary tract,megacystis, bilateral hydroureteronephrosis), and the absence of abdominal musculature. Routine screening during the antenatalperiod with ultrasound helps in detecting anomalies of the kidney at an earlier stage . This help in initiating optimal treatment toavoid the fatal cause of Prune Belly Syndrome