Cystic fibrosis: a mucosal immunodeficiency syndrome
Author:
Publisher
Springer Science and Business Media LLC
Subject
General Biochemistry, Genetics and Molecular Biology,General Medicine
Link
http://www.nature.com/articles/nm.2715.pdf
Reference191 articles.
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3. Knowles, M.R. et al. Ion composition of airway surface liquid of patients with cystic fibrosis as compared with normal and disease-control subjects. J. Clin. Invest. 100, 2588–2595 (1997).
4. Matsui, H. et al. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell 95, 1005–1015 (1998).
5. Martens, C.J. et al. Mucous solids and liquid secretion by airways: studies with normal pig, cystic fibrosis human, and non-cystic fibrosis human bronchi. Am. J. Physiol. Lung Cell. Mol. Physiol. 301, L236–L246 (2011).
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