Cysteamine therapy: a treatment for cystinosis, not a cure
Author:
Publisher
Elsevier BV
Subject
Nephrology
Reference14 articles.
1. Cystinosin, the protein defective in cystinosis, is a H(+)-driven lysosomal cystine transporter;Kalatzis;EMBO J,2001
2. Cystinosis: a disorder of lysosomal membrane transport;Gahl,2001
3. Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivo;Thoene;J Clin Invest,1976
4. Nephropathic cystinosis in adults: natural history and effects of oral cysteamine therapy;Gahl;Ann Intern Med,2007
5. Nephropathic cystinosis: late complications of a multisystemic disease;Nesterova;Pediatr Nephrol,2008
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