New insights into cystic fibrosis: molecular switches that regulate CFTR
Author:
Publisher
Springer Science and Business Media LLC
Subject
Cell Biology,Molecular Biology
Link
http://www.nature.com/articles/nrm1949.pdf
Reference105 articles.
1. Davis, P. B. Cystic fibrosis since 1938. Am. J. Respir. Crit. Care Med. 173, 475–482 (2006).
2. Wang, X., Kim, J., McWilliams, R. & Cutting, G. R. Increased prevalence of chronic rhinosinusitis in carriers of a cystic fibrosis mutation. Arch. Otolaryngol. Head Neck Surg. 131, 237–240 (2005).
3. Cohn, J. A. et al. Increased risk of idiopathic chronic pancreatitis in cystic fibrosis carriers. Human Mutat. 26, 303–307 (2005).
4. Bradbury, N. A. Intracellular CFTR: localization and function. Physiol. Rev. 79, S175–S191 (1999).
5. Bertrand, C. A. & Frizzell, R. A. The role of regulated CFTR trafficking in epithelial secretion. Am. J. Physiol. Cell Physiol. 285, C1–C18 (2003). An excellent review of PKA regulation of CFTR trafficking.
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