Targeting DNAJB9, a novel ER luminal co-chaperone, to rescue ΔF508-CFTR
Author:
Funder
U.S. Department of Health & Human Services | NIH | National Institute of Diabetes and Digestive and Kidney Diseases
Publisher
Springer Science and Business Media LLC
Subject
Multidisciplinary
Link
http://www.nature.com/articles/s41598-019-46161-4.pdf
Reference63 articles.
1. Ruggiano, A., Foresti, O. & Carvalho, P. Quality control: ER-associated degradation: protein quality control and beyond. J Cell Biol 204, 869–879, https://doi.org/10.1083/jcb.201312042 (2014).
2. Brodsky, J. L. The protective and destructive roles played by molecular chaperones during ERAD (endoplasmic-reticulum-associated degradation). Biochem J 404, 353–363, https://doi.org/10.1042/BJ20061890 (2007).
3. Kim, S. J. & Skach, W. R. Mechanisms of CFTR Folding at the Endoplasmic Reticulum. Front Pharmacol 3, 201, https://doi.org/10.3389/fphar.2012.00201 (2012).
4. Varga, K. et al. Efficient intracellular processing of the endogenous cystic fibrosis transmembrane conductance regulator in epithelial cell lines. J Biol Chem 279, 22578–22584, https://doi.org/10.1074/jbc.M401522200 (2004).
5. Ward, C. L. & Kopito, R. R. Intracellular turnover of cystic fibrosis transmembrane conductance regulator. Inefficient processing and rapid degradation of wild-type and mutant proteins. J Biol Chem 269, 25710–25718 (1994).
Cited by 18 articles. 订阅此论文施引文献 订阅此论文施引文献,注册后可以免费订阅5篇论文的施引文献,订阅后可以查看论文全部施引文献
1. Dynamic A-to-I RNA editing during acute neuroinflammation in sepsis-associated encephalopathy;Frontiers in Neuroscience;2024-08-02
2. COPII cage assembly factor Sec13 integrates information flow regulating endomembrane function in response to human variation;Scientific Reports;2024-05-03
3. Functional Consequences of CFTR Interactions in Cystic Fibrosis;International Journal of Molecular Sciences;2024-03-16
4. Nucleoporin downregulation modulates progenitor differentiation independent of nuclear pore numbers;Communications Biology;2023-10-18
5. CFTR Folding: From Structure and Proteostasis to Cystic Fibrosis Personalized Medicine;ACS Chemical Biology;2023-09-20
1.学者识别学者识别
2.学术分析学术分析
3.人才评估人才评估
"同舟云学术"是以全球学者为主线,采集、加工和组织学术论文而形成的新型学术文献查询和分析系统,可以对全球学者进行文献检索和人才价值评估。用户可以通过关注某些学科领域的顶尖人物而持续追踪该领域的学科进展和研究前沿。经过近期的数据扩容,当前同舟云学术共收录了国内外主流学术期刊6万余种,收集的期刊论文及会议论文总量共计约1.5亿篇,并以每天添加12000余篇中外论文的速度递增。我们也可以为用户提供个性化、定制化的学者数据。欢迎来电咨询!咨询电话:010-8811{复制后删除}0370
www.globalauthorid.com
TOP
Copyright © 2019-2024 北京同舟云网络信息技术有限公司 京公网安备11010802033243号 京ICP备18003416号-3