Differential overexpression of SERPINA3 in human prion diseases

Author:

Vanni S.ORCID,Moda F.,Zattoni M.,Bistaffa E.,De Cecco E.,Rossi M.,Giaccone G.,Tagliavini F.,Haïk S.,Deslys J. P.,Zanusso G.,Ironside J. W.,Ferrer I.,Kovacs G. G.ORCID,Legname G.ORCID

Publisher

Springer Science and Business Media LLC

Subject

Multidisciplinary

Reference60 articles.

1. Prusiner, S. B. Biology and genetics of prions causing neurodegeneration. Annu Rev Genet 47, 601–623, https://doi.org/10.1146/annurev-genet-110711-155524 (2013).

2. Collee, J. G., Bradley, R. & Liberski, P. P. Variant CJD (vCJD) and bovine spongiform encephalopathy (BSE): 10 and 20 years on: part 2. Folia Neuropathol 44, 102–110 (2006). doi:6212 [pii].

3. Mok, T. et al. Variant Creutzfeldt-Jakob Disease in a Patient with Heterozygosity at PRNP Codon 129. N Engl J Med 376, 292–294, https://doi.org/10.1056/NEJMc1610003 (2017).

4. Gill, O. N. et al. Prevalent abnormal prion protein in human appendixes after bovine spongiform encephalopathy epizootic: large scale survey. BMJ 347, f5675, https://doi.org/10.1136/bmj.f5675 (2013).

5. Advisory Committee on Dangerous Pathogens TSE Risk Assessment Subgroup (August 2016). “Appendix-III” position statement. Available from: ACDP TSE subgroup minutes, agendas and papers, https://app.box.com/s/hhhhg857fjpu2bnxhv6e (2016).

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