Prolonged co-treatment with HGF sustains epithelial integrity and improves pharmacological rescue of Phe508del-CFTR
Author:
Publisher
Springer Science and Business Media LLC
Subject
Multidisciplinary
Link
http://www.nature.com/articles/s41598-018-31514-2.pdf
Reference64 articles.
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2. Elborn, J. S. Cystic fibrosis. Lancet Lond. Engl. 388, 2519–2531 (2016).
3. Harutyunyan, M. et al. Personalized Medicine in CF: From Modulator Development to Therapy for Cystic Fibrosis Patients with Rare CFTR Mutations. Am. J. Physiol. Lung Cell. Mol. Physiol. https://doi.org/10.1152/ajplung.00465.2017 (2017).
4. Ren, C. L. et al. Cystic Fibrosis Pulmonary Guidelines: Use of CFTR Modulator Therapy in Patients with Cystic Fibrosis. Ann. Am. Thorac. Soc. https://doi.org/10.1513/AnnalsATS.201707-539OT (2018).
5. Char, J. E. et al. A little CFTR goes a long way: CFTR-dependent sweat secretion from G551D and R117H-5T cystic fibrosis subjects taking ivacaftor. PloS One 9, e88564 (2014).
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