Desmoplastic Fibroma of the Cranium: Case Report and Review of the Literature

Abstract

AbstractOBJECTIVE AND IMPORTANCEDesmoplastic fibroma is a benign bone tumor that can be locally aggressive. It usually occurs in the long bones and mandible. We report on a patient with a desmoplastic fibroma arising in the temporal bone and review previously published cases of desmoplastic fibroma originating within the cranium.CLINICAL PRESENTATIONA 43-year-old woman presented with a 12-year history of progressively worsening head asymmetry. Magnetic resonance imaging and computed tomography demonstrated a mass originating from the bone and involving the adjacent soft tissues.INTERVENTIONA temporal parietal craniectomy was performed with excision of a large tumor involving the bone. An acrylic cranioplasty was used to replace the bone. Pathological examination of the lesion identified desmoplastic fibroma of the cranium. After surgery, the patient's cranial asymmetry was corrected.CONCLUSIONDesmoplastic fibroma of the cranium is rare. Surgical resection is the treatment of choice.