Tripeptidyl-peptidase I deficiency in classical late-infantile neuronal ceroid lipofuscinosis brain tissue. Evidence for defective peptidase rather than proteinase activity-Reference-Cited by-同舟云学术

Tripeptidyl-peptidase I deficiency in classical late-infantile neuronal ceroid lipofuscinosis brain tissue. Evidence for defective peptidase rather than proteinase activity

Published:2000-03 Issue:2 Volume:23 Page:145-154
ISSN:0141-8955
Container-title:Journal of Inherited Metabolic Disease
language:en
Short-container-title:J Inherit Metab Dis

Author:

Warburton M. J.¹,Bernardini F.¹

Affiliation:

1. ; Department of Histopathology; St George's Hospital Medical School; London SW17 0RE UK

Publisher

Wiley

Subject

Genetics (clinical),Genetics

Link

http://onlinelibrary.wiley.com/wol1/doi/10.1023/A:1005665732189/fullpdf

Reference17 articles.

1. Specific delay in the degradation of mitochondrial ATP synthase subunit c in late infantile neuronal ceroid lipofuscinosis is derived from cellular proteolytic dysfunction rather than structural alteration of subunit c.;Ezaki;J Neurochem,1996

2. A giant protease with potential to substitute for some functions of the proteasome.;Geier;Science,1999

3. The neuronal ceroid-lipofuscinoses. Recent advances.;Goebel;Brain Pathol,1998

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