Phenylketonuria: Tyrosine beyond the phenylalanine-restricted diet
Author:
Affiliation:
1. ; Department of Metabolic Diseases, Beatrix Children's Hospital; University Hospital of Groningen; The Netherlands
2. ; Division of Medical Genetics; Children's Hospital; Los Angeles California USA
Publisher
Wiley
Subject
Genetics(clinical),Genetics
Link
http://onlinelibrary.wiley.com/wol1/doi/10.1023/A:1005689232358/fullpdf
Reference25 articles.
1. Unsuccessful treatment of phenylketonuria with tyrosine;Batshaw;J Pediatr,1981
2. Reduction of cerebrospinal £uid phenylalanine after oral administration of valine, isoleucine, and leucine;Berry;Pediatr Res,1982
3. Valine, isoleucine and leucine. A new treat-ment for phenylketonuria;Berry;Am J Dis Child,1990
4. Genetic failure of fetal amino acid ‘justi¢cation’: a common basis for many forms of metabolic, nutritional, and ‘nonspeci¢c’ mental retardation;Bessman;J Pediatr,1972
5. Historical perspective: tyrosine and maternal phenylketonuria, welcome news;Bessman;Am J Clin Nutr,1998
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