Branched-chain L-amino acid metabolism in classical maple syrup urine disease after orthotopic liver transplantation-Reference-Cited by-同舟云学术

Branched-chain L-amino acid metabolism in classical maple syrup urine disease after orthotopic liver transplantation

Published:2000-12 Issue:8 Volume:23 Page:805-818
ISSN:0141-8955
Container-title:Journal of Inherited Metabolic Disease
language:en
Short-container-title:J Inherit Metab Dis

Author:

Bodner-Leidecker A.¹,Wendel U.²,Saudubray J-M.³,Schadewaldt P.¹

Affiliation:

1. ; Deutsches Diabetes Forschungsinstitut; Heinrich-Heine-Universität; Düsseldorf Germany

2. ; Kinderklinik; Heinrich-Heine-Universität; Düsseldorf Germany

3. ; Hôpital Necker-Enfants-Malades; Paris France

Publisher

Wiley

Subject

Genetics(clinical),Genetics

Link

http://onlinelibrary.wiley.com/wol1/doi/10.1023/A:1026708618507/fullpdf

Reference35 articles.

1. Whole body branched-chain L-amino acid oxidation in overnight fasted human subjects;Bodner;Isotopes Environ Health Stud,1997

2. Liver transplantation in classical maple syrup urine disease (MSUD): near normalization of branched-chain L-amino acid metabolism;Bodner;J Inherit Metab Dis,1998

3. Modulation of whole body protein metabolism, during and after exercise, by variation of dietary protein;Bowtell;J Appl Physiol,1998

4. Thiamine increases the specific activity of human liver branched-chain a-ketoacid dehydrogenases;Danner;Nature,1975

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