Polyunsaturated fatty acid deficiency during dietary treatment of very long-chain acyl-CoA dehydrogenase deficiency. Rescue with soybean oil

Author:

Ruiz-Sanz J. I.1,Aldamiz-Echevarria L.1,Arrizabalaga J.1,Aquino L.1,Jimeno P.1,Pérez-Nanclares G.1,Sanjurjo P.1

Affiliation:

1. Spain

Publisher

Wiley

Subject

Genetics(clinical),Genetics

Reference25 articles.

1. ESPGAN Committee on Nutrition;Aggett;Acta Pediatr Scand,1991

2. A novel disease with deficiency in mitochondrial very-long-chain acyl-CoA dehydrogenase;Aoyama;Biochem Biophys Res Commun,1993

3. Very long chain acyl-CoA dehydrogenase deficiency: identification of a new error of mitochondrial fatty acid oxidation by fibroblasts;Bertrand;Biochim Biophys Acta,1993

4. Very long chain CoA dehydrogenase deficiency: successful treatment of acute cardiomyopathy;Brown-Harrison;Biochem Mol Med,1996

5. Cornstarch therapy in type I glycogen storage disease;Chen;J Am Diet Assoc,1994

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