Benign to Malignant Hepatic Lesion Transformation in Abernethy Malformation-Reference-Cited by-同舟云学术

Benign to Malignant Hepatic Lesion Transformation in Abernethy Malformation

Published:2024-04 Issue:4 Volume:11 Page:e01307
ISSN:2326-3253
Container-title:ACG Case Reports Journal
language:en
Short-container-title:ACG Case Rep J

Author:

Tom Chloe K.¹,Ter-Oganesyan Ramon²,Shefali Chopra³,Kaur Navpreet⁴,Pace Jordan L.⁵,Rastegarpour Ali⁶,Genyk Yuri⁷,Kahn Jeffrey A.⁸

Affiliation:

1. Division of Gastrointestinal and Liver Diseases, University of Southern California, Los Angeles, CA, USA

2. Division of Vascular and Interventional Radiology, Department of Radiology, University of Southern California, Los Angeles, CA, USA

3. Department of Pathology, University of Southern California, Los Angeles, CA, USA

4. Department of Surgery, University of Southern California, Los Angeles, CA, USA

5. California University of Science and Medicine Colton, CA, USA

6. Department of Diagnostic Radiology, University of Southern California Los Angeles, CA, USA

7. Division of Hepatobiliary/Pancreatic and Abdominal Organ Transplant Surgery, University of Southern California Los Angeles, CA, USA

8. Division of Gastrointestinal and Liver Diseases and Liver Transplant Program, University of Southern California Los Angeles, CA, USA

Abstract

ABSTRACT Abernethy malformation or congenital extrahepatic portosystemic shunt is an extremely rare condition whereby the portomesenteric blood drains into a systemic vein and bypasses the liver through a complete or partial shunt. Severe complications include hyperammonemia and encephalopathy, benign and malignant liver tumors, and hepatopulmonary syndrome. We describe a case where a female adult diagnosed with congenital extrahepatic portosystemic shunt subsequently developed focal nodular hyperplasia and then hepatocellular carcinoma.

Publisher

Ovid Technologies (Wolters Kluwer Health)

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