Affiliation:
1. Dona Libânia Dermatology Center, Brazil
Abstract
Rosai-Dorfman disease is a benign, self-limited, idiopathic proliferative histiocytic disorder. It was first described in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with fever, polyclonal gammopathy and leukocytosis with neutrophilia. The skin is the most common site affected. Extranodal manifestations have been reported in 43% of cases. In this study, we report an atypical case of Rosai-Dorfman disease in a female with massive cutaneous manifestation on the thigh, associated with a minimal lymphadenopathy limited to the regional inguinal lymph nodes.
Reference9 articles.
1. Clinicopathologic challenge. Destombes-Rosai-Dorfman disease (DRDD) (sinushistiocytosis with massive lymphadenopathy);Becker M;Int J Dermatol,2008
2. Cutaneous Rosai-Dorfman disease;Landim FM;An Bras Dermatol,2009
3. Extranodal Rosai-Dorfman disease with cutaneous, ophthalmic and laryngeal involvement: report of a case treated with isotretinoin;Chang LY;Int J Dermatol,2002
4. A case of cutaneous Rosai-Dorfman disease refractory to imatinib therapy;Gebhardt C;Arch Dermatol,2009
5. Five case of cutaneous Rosai-Dorfman disease;Pitamber HV;Clin Exp Dermatol,2003
Cited by
6 articles.
订阅此论文施引文献
订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献
1. Haga usted el diagnóstico: parte I;Revista de la Asociación Colombiana de Dermatología y Cirugía Dermatológica;2024-06-27
2. Enfermedad de Rosai-Dorfman;Revista de la Asociación Colombiana de Dermatología y Cirugía Dermatológica;2024-06-27
3. Cutaneous Rosai‐Dorfman disease after Covid 19 vaccination treated with thalidomide;Dermatologic Therapy;2022-10-07
4. Cutaneous Rosai‐Dorfman disease in a 3‐year‐old boy;Pediatric Dermatology;2022-07-18
5. Rosai‐Dorfman disease successfully treated with thalidomide: A case report;Dermatologic Therapy;2019-07-02